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(All recipes are reprinted from by kind permission of the Maple Syrup Urine Disease Family Support Group)

Fruit Slush

1 qt. diced peaches
6 bananas, sliced
1-20 oz. can crushed pineapple
1/2 lb. red seedless grapes, halved
1 qt. diced pears
6 oz. frozen orange juice concentrate
1/2 c. sugar

Drain fruit, saving the juice. Add water to reserved juice to make 3 cups; stir in 1/2 cup sugar and orange concentrate until dissolved. Pour juice mixture over combined fruits and mix. Freeze in a shallow pan. Remove from freezer 1/2 hour before serving. 16 servings.

  Leucine Protein Calories
Per serving: 73 mg 1.5 g 256
Per recipe: 1168 mg 23.5 g 4100

Orange Julius

1/3 c. (2 oz.) frozen orange juice (undiluted)
1/2 t. vanilla
1/2 c. non-dairy creamer
6 ice cubes
1/4 c. sugar (white or brown)
1/2 c. water

Blend in a blender until thick and ice cubes are chopped fine.

  Leucine Protein Calories
Per recipe: 69 mg 0.6 g 518

Dream Dessert

1 box (4 1/2 oz) vanilla cook & serve pudding
1 (6 oz) box orange Jello
4 1/2 c. water
8 oz. Cool Whip

Combine pudding mix and water. Bring to a boil and cook 1 minute. Add Jello; chill till partially set. Fold in Cool Whip. Pour into serving dish and chill until set. Makes 8 servings.

  Leucine Protein Calories
Per serving: 105mg 2.4g 216
Note: Use low protein gelled dessert in place of Jello to reduce protein

Creamy Sorbet

1-8 oz. container of Cool Whip, thawed
1 pint sorbet (desired flavor)

With a mixer whip Cool Whip and sorbet together.
Freeze. Makes 8-1/2 cup servings.

  Leucine Protein Calories
Per serving: 54 mg 1.0 g 148
Per recipe:  7.6g 1180

Tastes Like Devil's Food Cake

1/2 cup sugar
1/4 cup Miracle Whip
2 T. Hershey's Cocoa (not instant)
1/2 cup cold water
1/2 cup (55gm) Wel-Plan baking mix
1/2 cup (55 gm) wheat starch
1 tsp. baking soda
1/4 tsp. salt
1/2 tsp. vanilla
1/2 package instant pudding (chocolate or vanilla)

Combine all ingredients.Pour into a greased 8"x 8" pan.
Bake 20 to 25 minutes. Yields 10 pieces.

  Leucine Protein Calories
Per piece 18mg - 108

Spicy Candied Yams

16 oz. can yams or sweet potatoes, drained
1/2 tsp. cinnamon
3 T. packed brown sugar
1/4 tsp. ginger
2 T. margarine or butter, cut into pieces
1/4 tsp. cloves
1/2 c. Rich's Coffee Rich
2/3 c. (26 gm) mini marshmallows

Mash sweet potatoes or yams in a 1 qt. casserole dish. Stir in brown sugar, margarine, Rich's Coffee Rich and spices. Top with marshmallows. Bake at 350°, uncovered for 15 minutes or microwave on 70% power for 5 minutes. Yield: 2 2/3 cups (670 gm) 1 serving is 31 gm (2 tablespoons)

  Leucine Protein Calories
Per (31 gm) serving: 20mg 0.3g 44


The MSUD Family Support Group is currently funding several research projects and we are proactively looking for researchers interested in developing new treatments or finding a cure for MSUD. Significant funding is necessary if we are to accomplish this goal.
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