This list of low protein products is intended as a reference and resource for parents and others involved with the care of persons with maple syrup urine disease (MSUD). Although not all-inclusive, information is believed to be correct as of October 2003. This dietary related information was updated May 2004. All dietary decisions should be made in consultation with medical professionals—contact your physician or registered dietitian (nutritionist).

Food Products     |     Nutritional Resources     |    MSUD Food List Booklet

Teacher's Guide      |      Low Protein Cookbooks      |      Other Items

Formulas (Medical Foods)

Food Products

Cambrooke Foods, LLC

2 Central Street
Framingham, MA 01701
Phone (direct): 508-782-2300
Phone (toll free): 866-4 low pro (456-9776)
Fax: 978-443-1318
Web site:

New Products being added continually. Nutrient information including leucine values available on all products.
Specialty bakery items
Meat alternatives
Breakfast foods
Dry Pastas and Rice
Fresh-filled pastas
Baking Mixes br /> Ready Meals
Camino proTM Metabolic Formulas

Low Protein School Lunch Program: Cambrooke has designed a new program which features the medical forms, menus, nutritional information and recipes to guide parents and school Food Service Departments through the process of supplying children with a nutritious low protein lunch. Contact them for a copy.

Cooking Demonstrations: Clinics and metabolic groups can contact Cambrooke Foods to schedule a low protein food demonstration which features products from Cambrooke Foods.

Cambrooke Foods has the Camino proTM metabolic formula for MSUD: The Camino proTM drinks and sorbet stix are single serve and complete with vitamins and minerals. They are designed to fit your lifestyle and offer many nutritional bonuses to meet today's nutritional guidelines and make getting your protein throughout the day easier and tastier.

Send a note from your doctor or dietitian giving Cambrooke permission to send you a Camino proTM sample. Get more information on products here.

Med Diet Labs

3600 Holly Lane N, Suite 80
Plymouth, MN 55447
Phone: 1-800-med-diet (800-633-3438)
Fax: 763-550-2022
Web site:

Monthly specials. Variety packs available. Nutrient information on all products. Leucine values available on some.
Baking mixes
Breads and crackers
Cookies and desserts
Tumble & Bake Coating Mix
Pasta and rice
Broth, soups, sauces, gravies
. . . many other products


Dietary Specialites

10 Leslie Court
Whippany, NJ 07981
Phone (toll free): 888-640-2800
Fax: 973-884-5907
Web site:

Be sure to include your phone number when placing an order.
dp Baking Mix
DP Wheat Starch
D.S. Bread Machine Mix
Breads & rolls
Pizza & shells
Imitation Macaroni and Cheese
D.S. Pastas

Quick-to-fix single serving packages:   OHZ in Sauce
  Spanish Rice

Bread, Rusks & Crackertoast
Sauce mixes
Wise Onion Rings
Vance's Darifree
Prono Gelled Dessert Mix
Peanut Butter Spread
Calorie Supplement
Cake Mixes
Egg Replacer


Applied Nutrition

10 Saddle Road
Cedar Knolls, NJ 07927
Phone: 800-605-0410
Fax: 973-361-6707
Web site:

Manufactures own products. Nutrient information including leucine values available on all products.
Energy Option Protein Free Bars
(chocolate, white chocolate, mint)
Chocolate Flavored Coated Raisins
White Chocolate Coated Cranberries


SHS North America

 P.O. Box 117
 Gaithersburg, MD 20884-0117
Phone: 800-365-7354
Fax: 301-795-2301
Web site:

Nutrient information including leucine values available on all products.
Loprofin Products (LP)
LP Baking Mix
LP Pasta (several types)
LP Crackers, sweet biscuits and wafers
LP Drink Mix (milk substitute)
LP Cereal Loops
Wel-Plan Baking Mix

Also see: Cookbook Section of this List


Taste Connections

Phone: 310-371-8861
Web site:
Web site:

The bread mix can be used to make bread, pizza shells, rolls, bagels, pita bread, pretzels, etc. The baking mix can be used in place of flour to make pancakes, tortillas, bread, pizza shells, cookies, etc. Malathy Ramanujam, from California, has an adult son with Homocystinuria. She formulated these products to provide quick and easily prepared low protein meals and plans to add more bake-ready mixes and other products soon. Malathy also gives food demonstrations.

Call from 8 a.m. to 8 p.m. Monday thru Friday and 8 a.m. to 5 p.m. on weekends pacific standard time.
TC-Bread mix
TC-Baking mix



 3750 Francis Hughes
Laval, Quebec
H7L 5A9 Canada
Phone: 800-363-DIET (3438)
Fax: 450-629-4781
Web site:
Rusks & Crackers
Baking mixes


Uncle Henry's Pretzel Bakery

1550 Bowmansville Rd.
PO Box 219
Bowmansville, PA 17507
Phone: 717-445-4690
Fax: 717-445-8334
Web site:

Nutrient information including leucine values available.
Low Protein Pretzels
(regular size; handmade)


Ener-G Foods

5960 First Avenue, South
PO Box 84487
Seattle, WA 98124-5787
Phone: 800-331-5222
Fax: 206-764-3398
Web site:

No minimum order; will mix cases. Recipe selection service available. Nutrient information including leucine values available.
LP Breads
LP Candies
Baking mixes
Cheeses (in chunks)
LP Bread Mix
Pizza Shells
Egg Replacer
LP Imitation Cheeses
George Washington Broths
Cheese crackers
Cookies, pretzels & chips
Darifree Beverage Mix


Specialty Food Shop
(Toronto, Canada)
Phone: 416-997-4360
Fax: 416-977-8394
Toll free: 800-737-7976  
(24 hours 7 days a week)
Web site:

This food shop is owned and operated by The Hospital for Sick Children in Toronto. The products are all approved by a professional advisory committee. The shop employs registered dietitians to help customers with food choices.
Aproten products
Cambrooke Foods products
Dietary Specialties products
Kingsmill Food Products
Ener-G Foods Products
Loprofin Products
Wel-Plan Making Mix
Washington's broth


PK Foods
Unit 270 Centennial Park
Centennial Avenue
Elstree Borehamwood
Herts WD6 3SS
Phone: 020 8953 4444
Fax: 020 8953 8285
Web site:

A doctor's prescription is needed to purchase these low protein foods. Order form available online. Translation service link available.
Baking Mix


ECO Diet News
Apdo. 371 Logroño. La Rioja...
teléfono 941. 23 66 12
fax 941. 24 51 40
maquinas de pan
platos preparados


Clínica en España proveedora de productos bajos en proteína
fax # 954-6131755

Muchos más productos disponibles.
mezcla para pan
sucedáneo de huevo
sucedáneo de leche

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Nutritional Resources
The mission of the founders of, Ami and Laura Assayag is to create web and PDA (personal digital assistant) diet management technology to answer the needs of people with chronic disorders requiring dietary restrictions, like MSUD. As a first step toward that goal, the web site was launched to provide help with diet management. The complete online and PDA diet management services are not developed yet, but currently includes other useful tools and information:

  • Food lists and calculators with protein and leucine information

  • Community message boards to share experiences with others

  • Scales, breadmakers and other small appliances

  • Information about specific disorders

  • Low protein recipes

  • A unique weekly cartoon will soon add a database where nutritional information on low protein foods from vendors is listed for easy searching and quick nutrient calculations. The list of foods is extensive and is useful with the leucine amounts listed. Keep checking this web site for additional information and items:

NutritionData generates nutrition facts labels and provides simplified nutritional analyses for all foods and recipes. Has excellent search feature. It is a great resource for information on low-protein food values and lists 999 foods low in leucine. Check this web site:

Bowes and Church's Food Values of Portions Commonly Used
Eighteenth Edition, revised by Jean A.T. Pennington Ph.d, R.D.;March 2004, published by Lippincott, Williams & Wilkins.

For a complete nutritional reference book, order this book used by dietitians. It has the complete nutrient content of almost all foods and includes leucine other amino acid values.

The Bowes and Church's Food Values of Portions Commonly Used is available from Barnes & Noble Booksellers online, or by calling the nearest Barnes & Noble and ordering it by phone. If you access the Barnes & Noble Web-site you can find the location and contact information for the store nearest you. It can also be ordered from Walden Books, and it is available online from A very valuable and helpful book for families and adults dealing with MSUD and other metabolic diseases.

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MSUD Food List Booklet

Dr. Rani Singh (a nutritionist at Emory University, Atlanta, Georgia) and colleagues compiled a handy, pocket-sized booklet designed especially for persons with MSUD. It lists a large number of foods with the measurement, weight, calories, protein, leucine, and number of exchanges for each food. The information in this compact 40-page 4" x 6" booklet also includes: how to figure exchanges and understand food labels, how to determine leucine values when protein only is listed, lists of free foods and foods to avoid, a sample menu and more. The cost for this MSUD Food List booklet is $10. This is a great, quick reference of a wide variety of foods. Click here for order form (PDF).

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Teacher's Guide

The Arizona Department of Health Services has a "Teacher's Guide to MSUD" available for $2.50 each. This new guide booklet is ideal to give to the teachers of children with MSUD. Make checks payable to the Arizona Department of Health Services. Send a note requesting the booklet to:

Arizona Department of Health Services
Nutrition & Chronic Disease Prevention Services
150 North 18th Ave. #310
Phoenix, AZ 85007-3228
Attn: Lee Renda

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Low Protein Cookbooks

Low Protein Cookery for PKU, Third Edition
$29.95 plus $4.50 shipping. Out of U.S.A. orders add $5.50 shipping. Add $1 shipping for each additional book (U.S. funds only). Illinois residents add 8.75% sales tax. Canada add 7% GST. Make check payable to University of Chicago Distribution Center and send to:

University of Chicago Distribution Center
11030 S. Langley Avenue
Chicago, IL 60628
Phone: 800-621-2736

NEW: Labels for PKU Cookbook
Irene Brakus, the grandmother of a child with MSUD, did an excellent job of making labels containing valuable information for the second and third editions of Low Protein Cookery for PKU. Each label lists the page number, the name of the recipe, the exact amount of leucine, isoleucine, valine and protein, and the number of calories in a serving size. The label also lists a CF which stands for conversion factor. Multiply the amount in a serving by the CF number to find the amount in the whole recipe. This is especially handy when making larger or smaller servings. These labels are made to attach to each recipe in the cookbook and provide all you need to make the cookbook as useful for MSUD as for PKU. Order these from Ms. Brakus at no charge.

Ms. Irene O Brakus
1900 Lakeside Ave. NW
Canton, OH 44708-2950
Phone:  330-580-9221

Nutrient Content of Recipes from Low Protein Cookery for PKU
This was adapted for diet treatment for MSUD lists leucine, isoleucine and valine values for each recipe in the cookbook. Available from author, Virginia Schuett for $8. Make checks payable to National PKU News. Send to:

National PKU News
6869 Woodlawn Avenue, NE#116
Seattle, WA 98115

Books Available From SHS

  • Low Protein Bread Machine Baking for PKU — $18

  • New 2nd Edition—Low protein Food List for PKU — $50
Consult SHS for shipping costs. Send order to:

SHS North America
PO Box 117
Gaithersburg, MD 20884
Phone: 888-567-7646
Fax: 301-795-2301

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Other Items

New England Connection

5 Jones Lane
East Sandwich, MA 02537
Phone and Fax: 508-888-2295
Web site:

Mail order service is run by John Sullivan, a parent volunteer. Special candies and treats available for holidays.

No Credit Cards. Prices include shipping & handling; express delivery additional. Allow 2 weeks for normal delivery.
Ohaus CS2000 Digital Gram Scale: measures in 1 gm increments up to 2000 grams. Ultimate in accuracy. $95.

Ohaus CS200 Digital Gram Scale: measures in .1 gm increments for extreme precision. For special diets and medicinal purposes. Only measures up to 200 grams. $95.

Polder 934-90 Digital Gram Scale: measures in 1 gm increments. $35.

Polder 937-90 Digital Gram Scale: measures in 1 gm increments. $50.

Bread machine Model TR560 – vertical loaf. $95.

No-Mess Dough Board: makes difficult Lo-Pro dough a snap to roll out. $25.

(free recipe packet on request)

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Formulas (Medical Foods)
Information about formulas is provided for reference only. Consult physicians, registered dietitians (nutritionists), or other medical professionals about dietary matters.

Applied Nutrition

10 Saddle Road
Cedar Knolls, NJ 07927
Phone: 800-605-0410
Fax: 973-361-6707
Web site:
 Complex MSUD – vanilla flavored for children over 1 year & adults

 Amino Acid Bar – formula supplement for children over 1 year & adults

Amino Acid Blend – supplemental amino acids to add to food or formula


Mead Johnson

 2400 West Lloyd Expressway
 Evansville, IN 47721-0001
 Phone: 812-429-6399
1-800-BABY123 (212-9123)
Web site:

Mead Johnson discontinued marketing the 500 g/can modular metabolic products including MSUD 1 and MSUD 2 in September, 2004. See the next listed supplier, Milupa North America, for information on these products.  
MSUD Diet Powder* – infants & children

BCAD 1 – infants & toddlers (new)

BCAD 2 – children & adults

*MSUD Diet Powder will continue to be available for about one year following the launch of BCAD 1. For more information, refer to their web site ( or contact the Metabolic Medical Affairs Department at or call


Milupa North America

22513 Gateway Center Drive
Clarksburg, MD 20871
Phone: 301-217-4160
Fax: 301-217-4161
Web site:
MSUD 1 – infantsz

MSUD 2 – children & adults


Ross Products Division

Abbott Laboratories
625 Cleveland Avenue
Columbus, OH 43215-1724
Phone: 800-227-5767
Web site:
Ketonex-1 – infants & toddlers

Ketonex-2 – children & adults


SHS International

PO Box 117
Gaithersburg, MD 20884
Phone: 800-365-7354
Fax: 301-795-2301

In accordance with the new recommendations published by the Food and Nutrition Board of the Institute of Medicine, SHS North America updated their Maxamum product line. Here are some of the new Maxamum product highlights:
  • Formulations in accordance with new recommendations for Dietary Reference Intakes.

  • New convenient packaging of the XPhe Maxamum (flavored and unflavored in sachet form. One sachet (50 gm of the powder, providing 20 gm equivalent) can easily be mixed with chilled water, eliminating any weighing or measuring.

  • New consumer-friendly mixing instructions.

  • SHS will continue to offer both current and new formulations for a limited time to ease patient adaptation to the new formulas. A two-can sample case of the new formulation will be available to patients.
MSUD Analog – newborn to 1 year

MSUD Maxamaid – 1 to 8 years

MSUD Maxamum – over 8 years & adults

MSUD Acerflex (pineapple flavored) – 1 to 10 year


VITAFLOW International, Ltd.

 11-15 Century Building
Summers Road
Liverpool L3 4BL
Phone: +44 ( 0 ) 151 709 9020      
Fax: +44 ( 0 ) 151 709 9727

Ireland - Distributed by Allphar Services Ltd., Belgrad Road, Dublin 24.
Phone: ( 0 )1 404 1600.

Australia - Distributed by VITAFLO
Australia Pty Ltd., 14 Neich Road,
Glenorie, NSW 2157.
Phone: 03 5777 3919

Scandinavia - Distributed by VITAFLO Scandinavia, Box 53063, 40014
Goteborg, Sweden.
Phone: +46 31 3351196

USA - Available from Cambrooke Foods,
2 Central Street, Framingham, MA 01701 Phone (direct): 508-782-2300
Phone (toll free): 866-4 low pro (456-9776)  
MSUD Express - a low volume drink designed especially for teenagers and young adults. Available in sachets of 25 grams; convenient and easy to make one drink at a time.

MSUD Gel - a low volume drink for children 1-10. Available in sachets of 20 grams; convenient and easy  to make one drink at a time.

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The information presented on this web site is for educational purposes. It does not replace medical consultation.
The MSUD (Maple Syrup Urine Disease) Family Support Group is not liable for the application of this information or any errors therein.

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